Perioperative management of cardiac surgery patients with factor XII deficiency - two case reports.
نویسندگان
چکیده
This paper presents two patients with factor XII deficiency, a rare coagulation disorder, who successfully underwent surgery with cardiopulmonary bypass (CPB) in Cardiac Surgery Clinic of the 4th Military Clinical Hospital in Wroclaw. Diagnosis, intra- and postoperative course as well as proposed management strategy are described.
منابع مشابه
Anesthetic management using peripheral nerve block in patients with factor XI deficiency: a case report
Factor XI deficiency is rare but may cause life-threatening bleeding during the perioperative period. The clinical manifestation of factor XI deficiency is characterized by bleeding tendency. This unpredictable bleeding tendency makes anesthetic management difficult. We report a case of a partial duodenectomy in a patient with factor XI deficiency. The patient was scheduled for duodenectomy bec...
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Factor XI (FXI) deficiency is a rare, inherited bleeding disorder that is typically asymptomatic and presents with unexpected bleeding after surgery or trauma. We present a patient with FXI deficiency that underwent total knee arthroplasty (TKA) under general anesthesia and received peripheral nerve blocks for postoperative analgesia. We also present a review of literature focused on presentati...
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Factor XI deficiency (Hemophilia C) is a very rare autosomal recessive bleeding disorder. Patients with factor XI deficiency do not typically show any spontaneous bleeding or specific symptoms. Sometimes those who have this disorder are identified during special situations such as trauma or surgery. Orthognathic surgery is particularly associated with a high bleeding risk. Therefore, great care...
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ورودعنوان ژورنال:
- Anaesthesiology intensive therapy
دوره 44 4 شماره
صفحات -
تاریخ انتشار 2012